Year XVI -N.10/2000

 

 

 

 

 

 

CURRICULUM

“Hypovision” is a term used to describe the bilateral, irreversible central and/or peripheral functional impairment that cannot be resolved by means of standard optical correction and which leads to different degrees of visual disability. It has a central retinal component associated with a macular lesion that mainly affects visual acuity and thus causes difficulties in near activities (reading, performing fine work, recognising facial physiognomies, etc.), and a peripheral component associated with an impairment of the retina and/or extramacular fibres that causes an alteration in the visual field and thus reduces the autonomy of movement of affected subjects.

From a clinical point of view, it is held that visual disability begins when visual acuity decreases to less than 3/10 and the reduction in the visual field exceeds 60%. Hypovision is considered mild, moderate or severe on the basis of the severity of the functional impairment (Tab. 1), and the sum of the scores attributed to peripheral and central hypovision defines the degree and score of global hypovision. With the support of the UIC, the Italian Hypovision Study Group (GISI) has developed a new classification of perimetric defects for pension purposes, and presented it to the Italian Parliament in the form of a White Paper.

It is worth pointing out here that the current legislation almost exclusively recognises only central and paracentral perimetric defects, whereas the new classification proposes three levels of severity (mild, moderate and severe) concerning both the central and peripheral deficits revealed by means of the indices of computerised perimetry or its equivalent (Zingirian M, Gandolfo E, 1998).

Hypovision and age-related macular degeneration

Age-related macular degeneration (AMD) is currently the most frequent cause of legally recognised blindness among the people aged more than 60 years in the Western world. No precise estimates are available concerning the prevalence of hypovision due to this disease, but the table 2 shows the distribution of AMD by level of visual acuity as revealed by an analysis of the 1989 UIC lists made by Milan’s National Research Council.

Visual rehabilitation and AMD

AMD causes central hypovision, which means people who are no longer capable of using the fovea for fixation purposes and who therefore have to learn how to “look” using a less sensitive part of the retina.

The position of the new fovea is defined by the size of the scotoma and, in order to avoid the need to use excessive magnifications and minimise the angle of eccentric fixation, it must be immediately outside the area of the scotoma because the greater the angle of eccentric fixation, the greater the magnification needed to allow the perception of images and the shorter the reading distance.

In AMD patients, the new fovea may be decentralised laterally (in the case of small scotomas of 1-2o) or vertically above or below larger scotomas. The preferential localisation of the new fixation site should be stimulated, which can be done by using the scotometry programme of a scanning laser ophthalmoscope (SLO) or by establishing connections between the healthy retinal areas (revealed by means of fluoroangiography) and the visual field, in order to control the decentralisation, verify the concordance of the two examinations and establish whether it is necessary to correct the process.

The rehabilitation of these patients needs to consider other aspects, such as the ability to follow the direction of fixation, ensure stability of fixation during movement, and allow searching and finding by means of explorations involving both head and eye movements. Given that they are elderly, it is also necessary to bear in mind the presence of head or hand tremors, attention and memory capacities, cognitive skills and the characteristics of learning processes.

After having completed the clinical evaluation (near and distant visual acuity, with correction of the refractive defect; the size and location of the scotoma; contrast and chromatic sensitivity), the rehabilitation programme must consider:

a) the pertinence of the needs expressed by the patients (the need to read correspondence is pertinent, whereas the need to drive is not);

b) the qualitative and quantitative prognosis concerning the possible reduction of the visual disability, which must be formulated in such a way as to satisfy the pertinent requirements of the patient;

c) once having prescribed the magnifying aid most appropropriate to each individual patient (also bearing in mind his/her real economic possibilities!), it is necessary to organise a suitable follow up in order to evaluate the stability of the results.

Computer programmes that store and process the data concerning the functional characteristics of subjects with hypovision have been on the market for some years, and are capable of evaluating the clinical evolution of the condition and indicating the best prescribable magnifying aid.

One of the most innovative programmes (Essilor) is based on a video technology that makes it possible to perform perimetric, microperimetric and scotometric examinations, and evaluate the preferential fixation.

It is also capable of evaluating the degree of magnification necessary, the exploitable reading field and the characteristics of the ocular saccades in order to recommend the most suitable rehabilitation treatment. Finally, instruments for improving the visual performances of the hypo-sighted have been developed. These are based on monitoring the bioelectrical activity of the retina and the occipital cortical areas by means of PERG and VEP, and allow an objective quantification of treatment-related recovery. They make use of a sound feedback that informs patients about the efficacy of their visual apparatus in such a way as to optimise treatment results. It has been estimated that, up to the end of 1999, only 1% of the patients with hypovision living in Lombardy had attended a visual rehabilitation centre.

Magnifying aids

Magnifying lenses

These are the simplest and most convenient aids and, in the case of mild hypovision, make it possible to read texts with normal-sized characters. It is advisable to use lenses with the lowest useful dioptic power insofar as this allows the use of lenses with a larger diameter. It needs to be borne in mind that the best performances of all lenses are reached under good lighting conditions which, by reducing relative scotomas, allow the use of lower degrees of magnification.

Magnifying lenses may be used manually or mounted on spectacles. The former make it easy to perform various activities. They must be placed over the text to be read and then raised with the convex side facing the patient, and may contain their own light source, be equipped with a support or have the form of a ruler.

They have the advantage of being cheap. There are both aspheric and aplanar lenses: the first can reach a dioptic power of 20 D (corresponding to a magnification of 5x) and the second a dioptic power of 40 D (corresponding to a magnification of 10x).

However, in the latter case, the size of the visual field, as well as the distances between the eye and the lens and between the lens and the page, are greatly reduced and thus cause visual fatigue when used for prolonged periods of time. The lenses mounted on spectacles are used by raising the text towards the eyepiece until the correct distance has been reached, keeping the convex part of the lens facing the page. There is the possibility of incorporating the optical correction of the patient (spherical and cylindrical), as well as a coloured filter if necessary.

Before prescribing this aid, it is worth checking for the presence of head tremor, because this may compromise the use. Spectacle-mounted magnifying lenses offer a larger visual field, are lighter (given their small size), give rise to few aberrations, and leave the hands free. The appropriateness of bilateral application depends on the functional condition of the two eyes and the necessary spheric addition. In the case of additions of up to 14 D, it is advisable to use bilateral correction and prisms with a nasal base (e.g. for an addition of 10 D, a prism of 10 D).

Monocular use is preferable in the case of functionally different eyes and additions of more than 14 D; the addition can be as much as 40 D, but the distance of application is extremely limited. Fibre optic enlargers have recently become available, which have a magnification power of 2-3x. They do not need to be focussed, can be kept tilted and are extremely manageable, but they cost more than traditional magnifying lenses. Finally, there are also comfortable and cheap mirror-based magnifiers, and still experimental liquid crystal versions.

Telescopic systems

Usable for both near and distant vision, the vast majority of telescopic systems are monocular although can also be used binocularly. The simplest is the Galilean system, which consists of two coaxially mounted lenses (a negative eyepiece positioned in front of the eye and a positive objective at the front) separated by a distance equal to the sum of their focal lengths.

The posterior focus of the positive lens coincides with the anterior focus of the negative lens in such a way that the rays parallel on entry also exit in parallel, thus producing direct images. In the case of Keplerian systems, the fact that both the eyepiece and objective are positive means that the images are upturned and need to be righted using a prism.

Keplerian telescopes have greater magnification power than their Galilean counterparts, which are suitable up to about 2.5x: at higher magnifications, the quality of the image worsens and the usable visual field becomes very small and not very practical. Keplerian systems are used for patients with a 10-degree tubular visual field whereas, if the visual field is larger, it is worth using a Galilean telescope despite its lower level of magnification because it encompasses a visual field of up to 30 degrees. Keplerian telescopes are heavier and more cumbersome but, for the same visual field, allow a near work distance that is twice that of Galilean telescopes.

The correction is applied binocularly for distant sight but, for close vision, it is better to adopt a monocular correction after having selected the functionally better eye and applied an opaque lens over the other. The distance magnification is fixed (1.8x) and the aid needs to be used at a fixed distance; in order to obtain the correction for near vision, it is sufficient to apply a positive lens. In the case of Galilean systems, these are pressure mounted or screwed onto a threaded ring; Keplerian systems can be equipped with a zoom lens for both distant and near focussing.

The majority of telescopic systems are mounted on spectacles, but hand-held models are also available.

Videomagnifiers

These are devices designed to aid reading and writing. They work by means of an optical electronic process that projects the images onto a video screen at the necessary magnification (from 3x to 60x), and can be used by the hypo-sighted whose visus is so poor that they cannot use other enlargement systems. Almost all of the models allow the contrast of the text and the brightness of the backgound to be adjusted, the transition from a negative to a positive imagement, and the selection of a green background in order to make reading more relaxing. The size and weight of these devices mean that they are stably installed in the home.

A number of special functions have been recently introduced in order to improve their use, including electronic diaphragms, lines for underlining the lines to read, and anti-dazzle and anti-reflective screens. In some models, the distance between the work surface and the reading head is sufficient to allow the use of a typewriter, the reading of very thick volumes, and the execution of manual work such as sewing or model making.

The new electronic technologies have allowed the development of systems with palm-sized videocameras, which are extremely versatile, portable and can be connected to normal televisions. Some models have pushbutton or pedal-controlled videocameras.

Finally, there are also some small and truly portable systems consisting of a manual microcamera and an enlarging screen just a little larger than a notebook, which can be powered by battery as well as via the mains supply. It is now possible to find software that can magnify PC programmes and thus allow the normal use of a computer, which can also be equipped with a voice processor.

(traduzione dell’autore)

Chiara Olga Pierrottet